| Haojie Li,Daoyu Hu,Lili Liang,Yao Hu,Zhen Li. Intestinal lymphangiectasia associated with chylothorax and multiple lower extremity arteriovenous malformation: A case report and literature review. Oncol Transl Med, 2015, 1: 177-180. |
| Intestinal lymphangiectasia associated with chylothorax and multiple lower extremity arteriovenous malformation: A case report and literature review |
| Received:June 18, 2015 Revised:July 27, 2015 |
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| KeyWord:Intestinal lymphangiectasia (IL); case report; CT; MRI |
| Author Name | Affiliation | E-mail | | Haojie Li | Departments of Radiology, Tongji Hospital, Tongji Medical College, Huazhong University of Science and Technology | 897891279@qq.com | | Daoyu Hu | Departments of Radiology, Tongji Hospital, Tongji Medical College, Huazhong University of Science and Technology | cjr.hudaoyu@vip.163.com | | Lili Liang | Departments of Radiology, Tongji Hospital, Tongji Medical College, Huazhong University of Science and Technology | 409114750@qq.com | | Yao Hu | Departments of Radiology, Tongji Hospital, Tongji Medical College, Huazhong University of Science and Technology | 2320577158@qq.com | | Zhen Li | Departments of Radiology, Tongji Hospital, Tongji Medical College, Huazhong University of Science and Technology | doclizhen@qq.com |
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| Abstract: |
| Intestinal lymphangiectasia (IL) is an uncommon protein losing enteropathy, characterized by small intestinal mucosa or serosa lymphangiectasia and intestine lymph loss. Currently, IL is a very rare disease in children or adults, with typical clinical symptoms including hypoalbuminemia, absolute lymphocyte reduction, ascites, edema, etc. We report a case of an adult with intestinal lymphatic ectasia accompanied by chylothorax and multiply arteriovenous malformations of the hip and lower extremity. CT and MRI revealed diffuse edema and thickening of the small intestine, accompanied by splenomegaly and pleural effusion. Extensive nodularity of lower ileum and the ileocecal region could be seen during intestinal endoscopy. Finally, small intestinal lamina propria lymphangiectasis was confirmed by pathological examination. To raise awareness of the disease, here we compare our case and those previously reported, and discuss the
diagnosis and management of IL. |
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